Sturge Weber Syndrome

  • Kazi Nilufar Moly Department of Ophthalmology, BSMMU
  • S.M. Abu Ahsan 250 Beded General Hospital, Dist Thakurgoan
  • Md. Shafiqul lslam Department of Ophthalmology, BSMMU
Keywords: Angioma, Nevus flammeus, Hemangioma, Phakomatosis, Sturge Weber Syndrome

Abstract

Sturge weber syndrome is a rare sporadic condition of mesodermal phacomatosis, also called encephalotrigeminal angio­matosis (synonyms : fourth phacomatosis or mother spot), is a neurocutaneous disorder with angiomas that involve the leptomeninges (leptomeningeal angiomas) and the skin of the face (purple colored flat cutaneous haemangiomas ), typically in the ophthalmic (V1) and maxillary (V2) distributions of the trigeminal nerve. The hallmark of sturge weber syndrome is a facial cutaneous venous dilation, also referred to as a nevus flammeus or port wine stain (PWS). Because of the rarity, we report here a one & half year old male child who presented with features of the Sturge Weber Syndrome on both side of face.

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Author Biography

Kazi Nilufar Moly, Department of Ophthalmology, BSMMU

 

 

Published
2016-07-26
How to Cite
Moly, K., Ahsan, S., & lslam, M. (2016). Sturge Weber Syndrome. Bangabandhu Sheikh Mujib Medical University Journal, 8(1), 68-70. https://doi.org/10.3329/bsmmuj.v8i1.28924
Section
Case Reports