Moya Moya disease: Report of 2 cases and review of literature

  • MS Showkat Assistant Professor, Dept of Radiology & Imaging, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka
  • S Nuruzzaman Radiologist, Green Life Medical College and Hospital, Dhaka,
  • A Datta Dept of Radiology and Imaging. Bangabandhu Sheikh Mujib Medical University (BSMMU). Shahbag, Dhaka
Keywords: Moya moya, Cerebral vasculopathy, repeated headache, smoke appearance on imaging

Abstract

Moya moya disease is a chronic cerebral vasculopathy characterized by progressive occlusion of circle of Willis arteries that leads to development of collateral vessel which has a characteristic puff of smoke appearance on imaging. Here we described 2 cases, both were young and presented with history of stroke and repeated headache. In Magnetic Resonance Angiogram (MRA), we found marked narrowing in internal carotid, anterior, middle and posterior cerebral artery with multiple collaterals producing puff of smoke appearence which is the diagnostic imaging feature of Moya Moya disease. This is an important cause of repeated stroke in young patients. So physicians should be aware of this clinical entity.

DOI: http://dx.doi.org/10.3329/cbmj.v2i2.16705

Community Based Medical Journal 2013 July: Vol.02 No 02: 77-80

Downloads

Download data is not yet available.
Abstract
914
PDF
634
Published
2013-10-28
How to Cite
Showkat, M., Nuruzzaman, S., & Datta, A. (2013). Moya Moya disease: Report of 2 cases and review of literature. Community Based Medical Journal, 2(2), 78-80. https://doi.org/10.3329/cbmj.v2i2.16705
Section
Case Reports