Ectopia Cordis: A Rare Congenital Heart Disease

  • Naharuma Aive Hyder Chowdhury National Heart Foundation Hospital & Research & Institute, Dhaka
  • Mohammad Sharifuzzaman National Heart Foundation Hospital & Research & Institute, Dhaka
  • Mohammad Abul Kalam Azad National Heart Foundation Hospital & Research & Institute, Dhaka
  • Tuhin Haque National Heart Foundation Hospital & Research & Institute, Dhaka
  • Jesmin Hossain National Heart Foundation Hospital & Research & Institute, Dhaka
Keywords: Congenital heart disease, Ectopia cordis, Single ventricle.

Abstract

Three days old female presented with beating heart outside the thoracic cavity. This is a rare congenital abnormality associated multiple abnormalities. Patient came with features of infection. To diagnose routine blood investigation along with echocardiography and CT angiogram of heart,great vessel and abdomen were done. She was diagnosed as functionally single ventricle with hypoplastic branch pulmonary artery with malposed great artery with anomalous pulmonary venous drainage. Thisis lethal variety of ectopic cordis. Our patient had no adequate space in mediastinum to replace heart and she was in septicemia, so managed medically. Patient expired at her 6thday due to sepsis and intracardiac complex congenital heart disease.

Cardiovasc. j. 2019; 11(2): 183-186

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Abstract
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PDF
170
Published
2019-02-27
How to Cite
Chowdhury, N. A., Sharifuzzaman, M., Azad, M. A., Haque, T., & Hossain, J. (2019). Ectopia Cordis: A Rare Congenital Heart Disease. Cardiovascular Journal, 11(2), 183-186. https://doi.org/10.3329/cardio.v11i2.40419
Section
Case Reports