Reconstruction of the Sphenoid Wing in A Patient with Sphenoid Wing Dysplasia in NF1 – A Case Report

  • Tania Taher Assistant Professor HFRC Medical College Hospital
  • Kaisar Haroon Assistant professor, Department of Neurosurgery, NINSH
  • Shafiul Alam Associate Professor, Department of Neurosurgery, NINSH
  • Rakib Ul Haque Medical Officer, Department of Neurosurgery, NINSH
  • Sk Sader Hossain Professor and Head, Department of Neurosurgery, NINSH
Keywords: NF-Neurofibromatosis. CSF- cerebrospinal fluid

Abstract

Spheno-orbital dysplasia is almost pathognomic for Neurofibromatosis type 1. Thereis proptosis and deviation of the eye ball medially. We present a case of a young girlwith neurofibromatosis type 1, who had pulsating exophthalmos of the right eye withdiplopia and severe dysplasia of the sphenoid boneand consecutive herniation of theright temporal lobe. She presented with pulsatile proptosis and deviation of the righteye ball to the right. Her x-ray skull showed widening of the orbit. Her MRI scanshowed an arachnoid cyst behind her right eye ball. We had operated on her andreconstructed the right sphenoid greater wing with titanium mesh and duroplastywith G-patch. This had improved her proptosis and deviation of the eye ball.

Bang. J Neurosurgery 2020; 9(2): 156-161

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Abstract
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PDF
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Published
2020-01-14
How to Cite
Taher, T., Haroon, K., Alam, S., Haque, R., & Hossain, S. (2020). Reconstruction of the Sphenoid Wing in A Patient with Sphenoid Wing Dysplasia in NF1 – A Case Report. Bangladesh Journal of Neurosurgery, 9(2), 156-161. https://doi.org/10.3329/bjns.v9i2.44893
Section
Case Reports