Surgical experience with a huge supratentorial primitive neuroectodermal tumour in a 3 years old boy

Abstract

The concept of Primitive Neuroectodermal Tumor (PNET) has been evolving for many years, since its nomenclature has been done. A 3 years old boy presented with unable to stand and walk, vertigo, vomiting and visual disturbances. MRI of brain revealed suggestive of malignant tumour with intratumoral hemorrhage involving the frontotemporo- parietal region. A gross total removal of tumor was achieved through craniotomy. The pathological finding was consistent with PNET. This case is an exclusive one as it was huge size. Supratentorial PNETs are rare tumour and carry poor prognosis. Newer modalities of treatment should be tried to improve survival.

Key words: Supratentorial Primitive Neuroectodermal Tumour; Radiotherapy; Chemotherapy.

DOI: 10.3329/bjms.v9i3.6482

Bangladesh Journal of Medical Science Vol.09 No.3 July 2010, pp.177-182