Anaesthesia for a Patient with Gorham’s Disease A Very Rare Disease to Report

Authors

  • Nahida Parveen Nimmi Department of Anaesthesiology, Apollo Hospitals Dhaka, Bangladesh
  • Golam Ferdous Alam Department of Anaesthesiology, Apollo Hospitals Dhaka, Bangladesh
  • SP Mitra Department of Anaesthesiology, Apollo Hospitals Dhaka, Bangladesh
  • Lutful Aziz Department of Anaesthesiology, Apollo Hospitals Dhaka, Bangladesh

DOI:

https://doi.org/10.3329/jbsa.v29i2.65964

Keywords:

Gorham’s disease, Vanishing bone disease, Osteolysis, Airway management, Positioning

Abstract

Gorham disease, which is also known as massive osteolysis, vanishing bone disease or lymphangiomatosis, is an extremely rare condition, characterized by proliferation of vascular channels resulting in destruction and resorption of osseous matrix leading to bone loss, which in turn leads to joint instability and problems during airway management and positioning for surgery. Respiratory involvement may further complicate anaesthesia management. We are reporting the anaesthesia care of a 11-year-old boy of known GS with left sided chylothorax who came for amputation of left arm due to closed injury arm resulting from RTA.He was on cyclical Pamidronate therapy and had completed radiotherapy.

JBSA 2016; 29(2): 75-77

 

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Published

2016-07-01

How to Cite

Nimmi, N. P. ., Alam, G. F. ., Mitra, S., & Aziz, L. (2016). Anaesthesia for a Patient with Gorham’s Disease A Very Rare Disease to Report. Journal of the Bangladesh Society of Anaesthesiologists, 29(2), 75–77. https://doi.org/10.3329/jbsa.v29i2.65964

Issue

Section

Case Reports