Mayer-Rokytansky-kuster-Hauser Syndrome: A Rare Congenital Anomaly-Report of Two Cases

Authors

  • Roksana Parvin Phase B Resident, General Paediatrics, BSMMU, Dhaka, Bangladesh
  • Suraiya Begum Professor, Department of Paediatrics,BSMMU, Dhaka, Bangladesh
  • Romana Akhter Junior Consultant, Paediatrics, Infectious disease hospital, Dhaka, Bangladesh
  • Farzana Sharmin Phase B Resident, General Paediatrics, BSMMU, Dhaka, Bangladesh

DOI:

https://doi.org/10.3329/bjch.v45i1.55475

Keywords:

Mayer-Rokytansky- Kuster- Hauser Syndrome (MRKH), Mullerian duct, primary amenorrhea

Abstract

Mayer -Rokytansky-Kuster- Hauser Syndrome (MRKH) is a rare congenital anomaly, in which derivatives of mullerian duct is partially or completely absent whereas ovaries are normally present in a female patient. The patients usually present to physician with primary amenorrhea in adolescent period, when secondary sexual characteristics develops normally.Surgical correction permits normal sexual function and, possibly, reproduction with assisted techniques in MRKH patients. So,early diagnosis is very important to offer possible treatment options to the parents and patients and also to avoid psychological impact on patient. Here, we have described two cases of MRKH with different presenting complaints.

BANGLADESH J CHILD HEALTH 2021; VOL 45 (1) : 48-50

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Published

2021-09-05

How to Cite

Parvin, R. ., Begum, S. ., Akhter, R. ., & Sharmin, F. . (2021). Mayer-Rokytansky-kuster-Hauser Syndrome: A Rare Congenital Anomaly-Report of Two Cases. Bangladesh Journal of Child Health, 45(1), 48–50. https://doi.org/10.3329/bjch.v45i1.55475

Issue

Section

Case Reports